DermAtlas: Dermatology Image ip_1_020227 (incontinentia pigmenti

Dermatology - TRUNK: incontinentia pigmenti

Image Name:

ip_1_020227

File Type:

jpg

Diagnosis:

INCONTINENTIA PIGMENTI

Category:

hyperpigmentation /
genodermatosis/genetic disorder

Morphology:

Organization:

Pattern:

Color:

Body Site:

trunk

Age:

7 years

Gender:

female

Image Year:

2001

Contributor:

Camillo Di Cicco, MD,PhD

First Published:

February 27, 2002

Description:

A case of a 7 year old girl with swirled hyperpigmentation of the skin (trunk and extremities). In the newborn period she presented inflammatory lesions of the skin but she continues to grow and develop normally.

Comments:

This 7 year old girl demonstrates the swirled hyperpigmentation on the trunk and extremities typical of incontinentia pigmenti. Shortly after birth she developed linear urticarial papules and blisters, and a skin biopsy showed eosinophilic spongiosis in the epidermis. She has no serious complications from her disorder and continues to grow and develop normally.

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Other Resources:

PubMed: incontinentia pigmenti

OMIM: incontinentia pigmenti

MedlinePlus: incontinentia pigmenti

Archives of Dermatology: incontinentia pigmenti

eMedicine: incontinentia pigmenti

Dermatology Online: incontinentia pigmenti

Translation: