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Contributor

P. van Neer, MD

Diagnosis

granulomatous reaction ataxia-telangiectasia immunodeficiency, hereditary

Body Site

foot

Age

12 years

Pigmentation

light

Organization

grouped, clustered

Color

purple

Morphology

depressed (atrophy, loss of soft tissue,scar)

Pattern

asymmetric

Comments

This 12-year-old boy with ataxia-telangiectasia developed progressive violaceous fibrotic atrophic papules and plaques with overlying telangiectasias on his extremities and trunk. They continue to slowly increase in number and size.

Description

violaceous round fibrotic and atrophic plaques

Categories

granulomatous disorder lumps & bumps (plaques, nodules, tumors) atrophy

Image Added

2/2/2003 22:20:06

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Other Resources

PubMed Medline Plus Medscape

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