Mastocytosis, Urticaria Pigmentosa - DermAtlas

Contributor

Bill Abbottsmith

Diagnosis

mastocytosis urticaria pigmentosa

Body Site

trunk hand

Age

64 years

Pigmentation

medium

Organization

scattered

Color

red

Morphology

plaqulous (plaque / nodule / tumor)

Pattern

symmetric generalized, disseminated

Comments

This man was diagnosed with mastocytosis with a skin biopsy in 1990. A bone marrow biopsy from the right iliac crest showed an increased number of mast cells as well. Treatment with H1 (Chlorpheniramine 8mgm qid and H2 (Zantac 150mgm qid) together with Naproxen 500mgm bid (to block Prostaglandin D2) has been successful in preventing symptoms. However, for emergencies, theatient carries an EpiPen 0.3mgm for self treatment in severe flushing attacks which sometimes lead to anaphylaxis.

Description

widely disseminated reddish-brown papules predominantly on the knees, arms, and trunk

Image Added

5/24/2002 22:55:29

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Other Resources

PubMed Medline Plus Medscape

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