Klippel-Trenaunay-Weber Syndrome, Vascular Malformation - DermAtlas

Contributor

Russel Kirkby, MD

Diagnosis

Klippel-Trenaunay-Weber syndrome vascular malformation

Body Site

leg thigh knee

Age

46 years

Pigmentation

medium

Organization

confluent

Color

purple

Morphology

plaqulous (plaque / nodule / tumor)

Pattern

asymmetric

Comments

A 46-year-old woman with Klippel-Trenaunay_Weber syndrome syndrome had a below the knee amputation many years ago for limb atrophy and non healing ulcers. She developed chronic anemia from recurrent bleeding from blebs that developed on the stunp. The vascular malformation was also complicated by recurrent infections. Unfortunately the lesion extended into the retroperitoneal space and the bladder.

Description

diffuse purple patches studded with papules and nodules

Image Added

3/10/2005 23:18:17

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Other Resources

PubMed Medline Plus Medscape

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