Marfan Syndrome - DermAtlas - Dermatology Image Atlas

Contributor

Anthony Debartolome

Diagnosis

Marfan syndrome

Body Site

chest

Age

39 years

Pigmentation

Organization

Color

Morphology

Pattern

Comments

The most progressive cardiac lesion in Marfan syndrome is dilatation of the aorta, beginning at the aortic valve, and usually confined to the ascending portion. The valve ring is stretched resulting in severe aortic insufficiency. Dissecting aneurysm of the aorta with medial cystic necrosis and the development of aortic valvular incompetence may result in sudden death.

Description

aorta at surgery in a Marfan patient with aortic dilatation

Image Added

6/9/2004 8:11:37

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Other Resources

PubMed Medline Plus Medscape

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