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Contributor

Surajit Nayak, MD

Diagnosis

epidermolytic hyperkeratosis ichthyosis keratoderma, palmoplantar

Body Site

trunk sole palm

Age

35 years

Pigmentation

medium

Organization

discrete confluent

Color

yellow

Morphology

papulosquamous (bump, scale)

Pattern

acral (centripetal - extremity predominant) intertrigenous (creases) generalized, disseminated

Comments

This 35-year-old man had a history of widespread blistering since birth. He subsequently developed thickened scaly plaques on his palms, soles, and intertriginous areas. Epidermolytic hyperkeratosis was confirmed by a skin biopsy. His parents were second cousins.

Description

symmetric generalized thick scaly plaques with predominance on acral and intertriginous areas

Categories

genodermatosis/genetic disorder papulosquamous eruptions

Image Added

12/17/2005 15:10:17

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PubMed Medline Plus Medscape

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