Portwine Stain, Vascular Malformation - DermAtlas

Contributor

Bernard Cohen, MD

Diagnosis

portwine stain vascular malformation

Body Site

ear scalp

Age

4 years

Pigmentation

light

Organization

grouped, clustered

Color

red purple

Morphology

macular / flat (macule / patch)

Pattern

asymmetric

Comments

This healthy 4-year-old boy had a portwine stain involving his left ear and the surrounding parietal scalp. The left ear was somewhat hypertrophied, but no other abnormalities were present. His mother had a similar congenital vascular malformation involving her left ear, nearby parietal scalp and neck. Both mother and son had a few other small (less than 1 cm) portwine stains scattered at other sites on the trunk and extremities. Although many vascular malformations appear to be sporadic some, as in this family, are inherited in an autosomal dominant pattern.

Description

reddish-purple blanching patch

Image Added

2/17/2004 7:04:43

Translate

Other Resources

PubMed Medline Plus Medscape

Image Options

View Image in New Window