Hereditary Hemorrhagic Telangiectasia, Osler-Weber-Rendu Syndrome - DermAtlas

Contributor

Bernard Cohen, MD

Diagnosis

hereditary hemorrhagic telangiectasia Osler-Weber-Rendu syndrome

Body Site

lip tongue palate, hard

Age

70 years

Pigmentation

light

Organization

reticulated

Color

red purple

Morphology

plaqulous (plaque / nodule / tumor)

Pattern

symmetric

Comments

This 70 year old man began to develop telangiectasias on his ears, face, lips, tongue, and oral and nasal mucosae 25 years earlier. After extensive cautery of the nasal mucosa recurrent nose bleeds stopped about 10 years ago. He does experience persistent bleeding after accidental trauma to his face while shaving. Yellow pulsed dye laser therapy was scheduled for treatment of the cutaneous vascular telangiectasias. His family history was positive for similar vascular lesions in his sister, her children, his father, and several of his father's siblings.

Description

blanching round and reticulated reddish-purple plaques

Image Added

12/7/2002 23:31:46

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Other Resources

PubMed Medline Plus Medscape

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