Kindler Syndrome, Poikiloderma - DermAtlas

Contributor

Dawn Siegel, MD

Diagnosis

Kindler syndrome poikiloderma

Body Site

trunk arm chest abdomen

Age

21 years

Pigmentation

dark

Organization

Color

Morphology

depressed (atrophy, loss of soft tissue,scar)

Pattern

sun exposed areas

Comments

This is a 21 year old woman from Boscas del Toro, Panama with a history of congenital acral blisters and progressive poikiloderma. She has fragile skin that blisters after minor trauma and cigarette paper-like wrinkling of the hands and feet. She has photosensitivity resulting in erythema, pruritus and blisters. Her clinical findings and course are typical of Kindler syndrome, a rare autosomal recessive genodermatosis. These images were obtained with the help of Dr. Homero Penagos, Social Security Bureau of Panama.

Description

hyperpigmented and hypopigmented macules and patches and atrophy in sun exposed sites

Image Added

3/11/2001 20:52:28

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Other Resources

PubMed Medline Plus Medscape

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