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Contributor

Kosman Sadek Zikry, MD

Diagnosis

neurofibromatosis neurofibroma café au lait spot

Body Site

total body back

Age

40 years

Pigmentation

medium

Organization

mottled/speckled

Color

brown

Morphology

plaqulous (plaque / nodule / tumor)

Pattern

symmetric generalized, disseminated

Comments

This healthy 40-year-old woman had all of the cutaneous stigmata of neurofibromatosis including café au lait spots, intertriginous freckling, small cutaneous neurofibromas, plexiform neurofibromas, and Lisch nodules.

Description

disseminated 2 mm to 3 cm sharply demarcated brown macules and multiple scattered 1 cm to 4 cm subcutaenous soft compressible nodules and tumors

Categories

genodermatosis/genetic disorder lumps & bumps (plaques, nodules, tumors) hyperpigmentation

Image Added

6/7/2003 22:28:59

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Other Resources

PubMed Medline Plus Medscape

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