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Contributor

Shahbaz A. Janjua, MD

Diagnosis

scleroderma sclerodactyly

Body Site

hand finger

Age

8 years

Pigmentation

medium

Organization

confluent

Color

skin color brown

Morphology

fibrosis (scar, increased collagen)

Pattern

generalized, disseminated

Comments

This 8-year-old girl developed progressive systemic sclerosis with sclerodactyly. Scleroderma is a chronic, progressive dermatosis characterized by boardlike hardening and immobility of the affected skin and visceral involvement, particularly the lungs, esophagus, kidneys and heart. It may be accompanied by calcinosis, Raynaud's phenomenon, and telangiectasis (CREST syndrome). Acrosclerosis and sclerodactyly are comon findings. Childhood onset of progressive scleroderma is rare.

Description

generalized fibrotic bound down skin with loss of eye lashes, sparse eye brows and periorbital edema, erythema, and hyperpigmentation

Categories

collagen vascular disease clinical sign cutaneous sign of systemic disease

Image Added

2/18/2004 6:25:21

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Other Resources

PubMed Medline Plus Medscape

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