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Contributor

Bernard Cohen, MD

Diagnosis

smooth muscle and pilar hamartoma, congenital pseudo-Darier sign malformation, congenital nipple, accessory

Body Site

abdomen

Age

3 months

Pigmentation

light

Organization

Color

purple red

Morphology

plaqulous (plaque / nodule / tumor)

Pattern

asymmetric

Comments

This healthy infant had a curious congenital plaque with increased hair on his right lower abdomen/flank which became more prominent with rubbing. The pseudo-Darier sign was typical of a smooth muscle hamartoma.

Description

oval 10 X 4.5 cm slightly violaceous slightly indurated plaque with increased hair and increased prominence after rubbing

Categories

hair disorders neonatal dermatology congenital malformation

Image Added

5/30/2011 16:11:15

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Other Resources

PubMed Medline Plus Medscape

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